Hemodynamics Response to Upper Airway Obstruction in Marfan Syndrome
Completed · Not applicable
Conditions studied: Sleep-disordered Breathing, Snoring
In brief
Upper airway obstruction (UAO) is an unrecognized source of hemodynamic stress that may contribute to aortic adverse events in persons with Marfan Syndrome (MFS). UAO occurs during snoring and sleep apnea and is characterized by repetitive partial or complete obstruction of the upper airway during sleep. These obstructive breathing events lead to intermittent surges in blood pressure (BP) REF and large decreases in pleural pressure (Pes), thereby increasing the trans-mural aortic pressure (TMP) and imposing mechanical stress on the aorta during sleep. Although UAO is known to increase mechanical stress on the aorta, the magnitude of the increase is not known for persons with MFS. In this project, therefore, the investigators will also examine the changes in Pes and BP responses in periods of obstructed breathing and compare the diurnal markers or vascular stress between Baseline and CPAP studies in MFS persons.
Key facts
- Study ID
- NCT03985657
- Run by
- Johns Hopkins University
- People needed
- 31
- Starts
- 2018-06-06
- Expected to finish
- 2019-12-06
- Last updated by the study team
- 2020-12-28
Who can join
Age: 18 and older. Sex: any. Healthy volunteers: accepted.
You may qualify if…
- People with Marfan syndrome.
- Age ≥ 18yrs
- Able and willing to provide informed consent
- Willing to sleep connected to research apparatus
You may not qualify if…
- Unstable cardiovascular disease (CHF, myocardial infarction or revascularization procedures, and unstable arrhythmias)
- Uncontrolled hypertension (BP > 190/110)
- Underlying obstructive or other intrinsic lung disease
- Renal failure on dialysis
- Cirrhosis
- Pregnancy
Where it is running
- Johns Hopkins University — Baltimore, Maryland, United States
Full record on ClinicalTrials.gov
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