Genetic Analysis of Oculocerebrorenal Syndrome of Lowe

Completed

Conditions studied: Lowe Syndrome

In brief

This study will investigate the genetic basis of oculocerebrorenal syndrome of Lowe (OCRL)-a rare X-linked disorder (carried by females and passed to males). Patients with OCRL have abnormal development of the eye lens, developmental delay, muscle weakness and kidney dysfunction. The study will examine DNA and cell samples obtained and archived from patients with OCRL enrolled in a previous protocol (HG008A) between 1996 and 1999. It will identify mutations in the OCRL1 gene responsible for OCRL in affected males and try to correlate them with specific biochemical or cellular activities (e.g., enzyme activity, protein stability, cellular localization and trafficking). When test results are available, the information will be communicated to the patients, their parents (if the patient is a minor) and their physicians, and families will receive genetic counseling.

Key facts

Study ID
NCT00359515
Run by
National Human Genome Research Institute (NHGRI)
People needed
120
Starts
2001-02-17
Expected to finish
2009-02-03
Last updated by the study team
2017-07-02

Who can join

Age: any. Sex: male. Healthy volunteers: not accepted.

Where it is running

Full record on ClinicalTrials.gov

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